Lecturer

Dr Georg Von Jonquieres

Medicine & Health
School of Biomedical Sciences
Phone
+61 2 9385 2376
  • Journal articles | 2022
    Cederholm JME; Parley KE; Perera CJ; von Jonquieres G; Pinyon JL; Julien JP; Ryugo DK; Ryan AF; Housley GD, 2022, 'Noise-induced hearing loss vulnerability in type III intermediate filament peripherin gene knockout mice', Frontiers in Neurology, vol. 13, pp. 962227, http://dx.doi.org/10.3389/fneur.2022.962227
    Journal articles | 2021
    Eykens C; Rossaert E; Duqué S; Rué L; Bento-Abreu A; Hersmus N; Lenaerts A; Kerstens A; Corthout N; Munck S; Van Damme P; Holt MG; von Jonquires G; Klugmann M; Van Den Bosch L; Robberecht W, 2021, 'AAV9-mediated gene delivery of MCT1 to oligodendrocytes does not provide a therapeutic benefit in a mouse model of ALS', Molecular Therapy - Methods and Clinical Development, vol. 20, pp. 508 - 519, http://dx.doi.org/10.1016/j.omtm.2021.01.006
    Journal articles | 2021
    von Jonquieres G; Rae CD; Housley GD, 2021, 'Emerging Concepts in Vector Development for Glial Gene Therapy: Implications for Leukodystrophies', Frontiers in Cellular Neuroscience, vol. 15, http://dx.doi.org/10.3389/fncel.2021.661857
    Journal articles | 2020
    Brown CN; Fultz EK; Ferdousian S; Rogers S; Lustig E; Page A; Shahin JR; Flaherty DM; Von Jonquieres G; Bryant CD; Kippin TE; Szumlinski KK, 2020, 'Transgenic Analyses of Homer2 Function Within Nucleus Accumbens Subregions in the Regulation of Methamphetamine Reward and Reinforcement in Mice', Frontiers in Psychiatry, vol. 11, http://dx.doi.org/10.3389/fpsyt.2020.00011
    Journal articles | 2020
    Housley DM; Pinyon JL; Von Jonquieres G; Perera CJ; Smout M; Liddell MJ; Jennings EA; Wilson D; Housley GD, 2020, 'Australian scorpion Hormurus waigiensis venom fractions show broad bioactivity through modulation of bio-impedance and cytosolic calcium', Biomolecules, vol. 10, http://dx.doi.org/10.3390/biom10040617
    Journal articles | 2020
    Housley GD; von Jonquieres G; Pinyon JL; Matheson JAT; Pearson LJ; Salthouse TP; Cederholm JM, 2020, 'Cochlear homeostasis: a molecular physiological perspective on maintenance of sound transduction and auditory neurotransmission with noise and ageing', Current Opinion in Physiology, vol. 18, pp. 106 - 115, http://dx.doi.org/10.1016/j.cophys.2020.09.012
    Journal articles | 2020
    Richards LA; Kumari A; Knezevic K; Thoms JAI; von Jonquieres G; Napier CE; Ali Z; O'Brien R; Marks-Bluth J; Maritz MF; Pickett HA; Morris J; Pimanda JE; MacKenzie KL, 2020, 'DKC1 is a transcriptional target of GATA1 and drives upregulation of telomerase activity in normal human erythroblasts', Haematologica, vol. 105, pp. 1517 - 1526, http://dx.doi.org/10.3324/haematol.2018.215699
    Journal articles | 2019
    Campbell RR; Domingo RD; Williams AR; Wroten MG; McGregor HA; Waltermire RS; Greentree DI; Goulding SP; Thompson AB; Lee KM; Quadir SG; Chavez CLJ; Coelho MA; Gould AT; Von Jonquieres G; Klugmann M; Worley PF; Kippin TE; Szumlinski KK, 2019, 'Increased alcohol-drinking induced by manipulations of mGlu5 phosphorylation within the bed nucleus of the stria terminalis', Journal of Neuroscience, vol. 39, pp. 2745 - 2761, http://dx.doi.org/10.1523/JNEUROSCI.1909-18.2018
    Journal articles | 2019
    Cederholm JME; Kim Y; von Jonquieres G; Housley GD, 2019, 'Human Brain Region-Specific Alternative Splicing of TRPC3, the Type 3 Canonical Transient Receptor Potential Non-Selective Cation Channel', Cerebellum, http://dx.doi.org/10.1007/s12311-019-01026-4
    Journal articles | 2019
    Pinyon JL; von Jonquieres G; Crawford EN; Duxbury M; Al Abed A; Lovell NH; Klugmann M; Wise AK; Fallon JB; Shepherd RK; Birman CS; Lai W; McAlpine D; McMahon C; Carter PM; Enke YL; Patrick JF; Schilder AGM; Marie C; Scherman D; Housley GD, 2019, 'Neurotrophin gene augmentation by electrotransfer to improve cochlear implant hearing outcomes', Hearing Research, vol. 380, pp. 137 - 149, http://dx.doi.org/10.1016/j.heares.2019.06.002
    Journal articles | 2018
    Broccoli L; Uhrig S; von Jonquieres G; Schönig K; Bartsch D; Justice NJ; Spanagel R; Sommer WH; Klugmann M; Hansson AC, 2018, 'Targeted overexpression of CRH receptor subtype 1 in central amygdala neurons: effect on alcohol-seeking behavior', Psychopharmacology, vol. 235, pp. 1821 - 1833, http://dx.doi.org/10.1007/s00213-018-4908-6
    Journal articles | 2018
    Fröhlich D; Suchowerska AK; Voss C; He R; Wolvetang E; Von Jonquieres G; Simons C; Fath T; Housley GD; Klugmann M, 2018, 'Expression pattern of the aspartyl-tRNA synthetase DARS in the human brain', Frontiers in Molecular Neuroscience, vol. 11, http://dx.doi.org/10.3389/fnmol.2018.00081
    Journal articles | 2018
    Powell KL; Fitzgerald X; Shallue C; Jovanovska V; Klugmann M; Von Jonquieres G; O'Brien TJ; Morris MJ, 2018, 'Gene therapy mediated seizure suppression in Genetic Generalised Epilepsy: Neuropeptide Y overexpression in a rat model', Neurobiology of Disease, vol. 113, pp. 23 - 32, http://dx.doi.org/10.1016/j.nbd.2018.01.016
    Journal articles | 2018
    von Jonquieres G; Spencer ZHT; Rowlands BD; Klugmann CB; Bongers A; Harasta AE; Parley KE; Cederholm J; Teahan O; Pickford R; Delerue F; Ittner LM; Fröhlich D; McLean CA; Don AS; Schneider M; Housley GD; Rae CD; Klugmann M, 2018, 'Uncoupling N-acetylaspartate from brain pathology: implications for Canavan disease gene therapy', Acta Neuropathologica, vol. 135, pp. 95 - 113, http://dx.doi.org/10.1007/s00401-017-1784-9
    Journal articles | 2017
    Bi M; Gladbach A; Van Eersel J; Ittner A; Przybyla M; Van Hummel A; Chua SW; Hoven JVD; Lee WS; Müller J; Parmar J; Jonquieres GV; Stefen H; Guccione E; Fath T; Housley GD; Klugmann M; Ke YD; Ittner LM, 2017, 'Tau exacerbates excitotoxic brain damage in an animal model of stroke', Nature Communications, vol. 8, http://dx.doi.org/10.1038/s41467-017-00618-0
    Journal articles | 2017
    Datko MC; Hu JH; Williams M; Reyes CM; Lominac KD; von Jonquieres G; Klugmann M; Worley PF; Szumlinski KK, 2017, 'Behavioral and neurochemical phenotyping of mice incapable of homer1a induction', Frontiers in Behavioral Neuroscience, vol. 11, http://dx.doi.org/10.3389/fnbeh.2017.00208
    Journal articles | 2017
    Fröhlich D; Suchowerska AK; Spencer ZHT; von Jonquieres G; Klugmann CB; Bongers A; Delerue F; Stefen H; Ittner LM; Fath T; Housley GD; Klugmann M, 2017, 'In vivo characterization of the aspartyl-tRNA synthetase DARS: Homing in on the leukodystrophy HBSL', Neurobiology of Disease, vol. 97, pp. 24 - 35, http://dx.doi.org/10.1016/j.nbd.2016.10.008
    Journal articles | 2017
    Georgiou E; Sidiropoulou K; Richter J; Papaneophytou C; Sargiannidou I; Kagiava A; Von Jonquieres G; Christodoulou C; Klugmann M; Kleopa KA, 2017, 'Gene therapy targeting oligodendrocytes provides therapeutic benefit in a leukodystrophy model', Brain, vol. 140, pp. 599 - 616, http://dx.doi.org/10.1093/brain/aww351
    Journal articles | 2017
    Szumlinski KK; Lominac KD; Campbell RR; Cohen M; Fultz EK; Brown CN; Miller BW; Quadir SG; Martin D; Thompson AB; von Jonquieres G; Klugmann M; Phillips TJ; Kippin TE, 2017, 'Methamphetamine Addiction Vulnerability: The Glutamate, the Bad, and the Ugly', Biological Psychiatry, vol. 81, pp. 959 - 970, http://dx.doi.org/10.1016/j.biopsych.2016.10.005
    Journal articles | 2016
    O'Brien R; Tran SL; Maritz MF; Liu B; Kong CF; Purgato S; Yang C; Murray J; Russell AJ; Flemming CL; von Jonquieres G; Pickett HA; London WB; Haber M; Gunaratne PH; Norris MD; Perini G; Fletcher JI; MacKenzie KL, 2016, 'MYC-Driven Neuroblastomas Are Addicted to a Telomerase-Independent Function of Dyskerin', Cancer Research, vol. 76, pp. 3604 - 3617, http://dx.doi.org/10.1158/0008-5472.CAN-15-0879
    Journal articles | 2016
    von Jonquieres G; Fröhlich D; Klugmann CB; Wen X; Harasta AE; Ramkumar R; Spencer ZHT; Housley GD; Klugmann M, 2016, 'Recombinant human myelin-associated glycoprotein promoter drives selective AAV-mediated transgene expression in oligodendrocytes', Frontiers in Molecular Neuroscience, vol. 9, http://dx.doi.org/10.3389/fnmol.2016.00013
    Journal articles | 2015
    Gould AT; Sacramento AD; Wroten MG; Miller BW; Von Jonquieres G; Klugmann M; Ben-Shahar O; Szumlinski KK, 2015, 'Cocaine-elicited imbalances in ventromedial prefrontal cortex Homer1 versus Homer2 expression: Implications for relapse', Addiction Biology, vol. 20, pp. 148 - 157, http://dx.doi.org/10.1111/adb.12088
    Journal articles | 2015
    Harasta AE; Power JM; Von Jonquieres G; Karl T; Drucker DJ; Housley GD; Schneider M; Klugmann M, 2015, 'Septal glucagon-like peptide 1 receptor expression determines suppression of cocaine-induced behavior', Neuropsychopharmacology, vol. 40, pp. 1969 - 1978, http://dx.doi.org/10.1038/npp.2015.47
    Journal articles | 2014
    Cozzoli DK; Courson J; Wroten MG; Greentree DI; Lum EN; Campbell RR; Thompson AB; Maliniak D; Worley PF; Jonquieres G; Klugmann M; Finn DA; Szumlinski KK, 2014, 'Binge alcohol drinking by mice requires intact group1 metabotropic glutamate receptor signaling within the Central nucleus of the Amygdale', Neuropsychopharmacology, vol. 39, pp. 435 - 444, http://dx.doi.org/10.1038/npp.2013.214
    Journal articles | 2014
    Von Jonquieres G; Froud KE; Klugmann CB; Wong ACY; Housley GD; Klugmann M, 2014, 'Loss of central auditory processing in a mouse model of canavan disease', PLoS ONE, vol. 9, http://dx.doi.org/10.1371/journal.pone.0097374
    Journal articles | 2013
    Ary AW; Lominac KD; Wroten MG; Williams AR; Campbell R; Ben-shahar OM; Von Jonquieres G; Klugmann M; Szumlinski KK, 2013, 'Imbalances in prefrontal cortex CC-Homer1 versus CC-Homer2 expression promote cocaine preference', Journal of Neuroscience, vol. 33, pp. 8101 - 8113, http://dx.doi.org/10.1523/JNEUROSCI.1727-12.2013
    Journal articles | 2013
    Jonquieres G; Mersmann N; Teahan O; Klugmann CB; Harasta AE; Lutz B; Housley GD; Klugmann M, 2013, 'AAV-BASED GENE THERAPY APPROACHES FOR THE TREATMENT OF CANAVAN DISEASE', CYTOTHERAPY, vol. 15, pp. S12 - S12, http://dx.doi.org/10.1016/j.jcyt.2013.01.042
    Journal articles | 2013
    Obara I; Goulding SP; Gould AT; Lominac KD; Hu JH; Zhang PW; von Jonquieres G; Dehoff M; Xiao B; Seeburg PH; Worley PF; Klugmann M; Szumlinski KK, 2013, 'Homers at the interface between reward and pain', Frontiers in Psychiatry, vol. 4, http://dx.doi.org/10.3389/fpsyt.2013.00039
    Journal articles | 2013
    Von Jonquieres G; Mersmann N; Klugmann CB; Harasta AE; Lutz B; Teahan O; Housley GD; Frohlich D; Kramer-Albers EM; Klugmann M, 2013, 'Glial Promoter Selectivity following AAV-Delivery to the Immature Brain', PLoS ONE, vol. 8, pp. Article number e65646, http://dx.doi.org/10.1371/journal.pone.0065646
    Journal articles | 2013
    von Jonquieres G; Klugmann C; Harrasta A; Klugmann M, 2013, 'DEVELOPMENT OF RAAV VECTORS FOR THE TREATMENT OF LEUKODYSTROPHIES', CYTOTHERAPY, vol. 15, pp. S33 - S33, http://dx.doi.org/10.1016/j.jcyt.2013.01.125
    Journal articles | 2011
    Thoms JAI; Birger Y; Foster S; Knezevic K; Kirshenbaum Y; Chandrakanthan V; Jonquieres G; Spensberger D; Wong JW; Oram SH; Kinston SJ; Groner Y; Lock RB; MacKenzie KL; Gottgens B; Izraeli S; Pimanda JE, 2011, 'ERG promotes T-acute lymphoblastic leukemia and is transcriptionally regulated in leukemic cells by a stem cell enhancer', Blood, vol. 117, pp. 7079 - 7089, http://dx.doi.org/10.1182/blood-2010-12-317990
    Journal articles | 2010
    Marshall GM; Gherardi S; Xu N; Neiron Z; Trahair TN; Scarlett CJ; Chang DK; Liu PY; Jankowski K; Iraci N; Haber M; Norris MD; Keating J; Sekyere E; Jonquieres G; Biankin AV; Stossi F; Katzenellenbogen BS; Perini G; Liu T, 2010, 'Transcriptional upregulation of histone deacetylase 2 promotes Myc-induced oncogenic effects', Oncogene, vol. 29, pp. 5957 - 5968, http://dx.doi.org/10.1038/onc.2010.332
    Journal articles | 2010
    Von Jonquieres G, 2010, 'Transcriptional upregulation of histone deacetylase 2 promotes Myc-induced oncogenic effects', Oncogene, vol. 29, pp. 5957 - 5968, http://dx.doi.org/10.1038/onc.2010.332
    Journal articles | 2009
    Von Jonquieres G, 2009, 'Hyperactivation of the Insulin-like Growth Factor Receptor I Signaling Pathway Is an Essential Event for Cisplatin Resistance of Ovarian Cancer Cells', Cancer Research, vol. 69, pp. 2996 - 3003, http://dx.doi.org/10.1158/0008-5472.CAN-08-3153
    Journal articles | 2008
    Von Jonquieres G, 2008, 'Acquired cisplatin resistance in the head–neck cancer cell line Cal27 is associated with decreased DKK1 expression and can partially be reversed by overexpression of DKK1', International Journal of Cancer, vol. 123, pp. 2013 - 2019, http://dx.doi.org/10.1002/ijc.23721
    Journal articles | 2008
    Von Jonquieres G, 2008, 'Epidermal growth factor receptor pathway analysis identifies amphiregulin as a key factor for cisplatin resistance of human breast cancer cells.', The Journal of Biological Chemistry, vol. 283, pp. 739 - 750, http://dx.doi.org/10.1074/jbc.M706287200
  • Preprints | 2021
    Cederholm JME; Parley KE; Perera CJ; von Jonquieres G; Pinyon JL; Julien J-P; Ryugo DK; Ryan AF; Housley GD, 2021, Association of cochlear outer hair cell - type II spiral ganglion afferents with protection from noise-induced hearing loss, http://dx.doi.org/10.1101/2021.11.06.467554
    Conference Abstracts | 2020
    Pearson L; Pinyon J; Von Jonquieres G; Cederholm J; Housley G, 2020, 'Characterising auditory neurons through transgene expression.', in Australasian Auditory Neuroscience Webinar, presented at Australasian Auditory Neuroscience Workshop
    Conference Abstracts | 2017
    von Jonquieres G; Klugmann C; Frohlich D; Housley GD; Klugmann M, 2017, 'NOVEL APPROACHES TO PREVENT THE NAASTY - TARGETED GENE THERAPY FOR LEUKODYSTROPHIES', in JOURNAL OF GENE MEDICINE, WILEY, AUSTRALIA, Univ Technol Sydney, Sydney, Vol. 20, presented at Joint 10th Annual Scientific Meeting of the Australian-Gene-and-Cell-Therapy-Society (AGCTS) and Australasian-Society-for-Stem-Cell-Research (ASSCR), AUSTRALIA, Univ Technol Sydney, Sydney, 24 May 2017 - 26 May 2017, https://www.webofscience.com/api/gateway?GWVersion=2&SrcApp=PARTNER_APP&SrcAuth=LinksAMR&KeyUT=WOS:000426528300030&DestLinkType=FullRecord&DestApp=ALL_WOS&UsrCustomerID=891bb5ab6ba270e68a29b250adbe88d1
    Conference Papers | 2016
    Georgiou E; Kagiava A; Sidiropoulou K; Richter J; Sargiannidou I; Papaneophytou C; von Jonquieres G; Christodoulou C; Klugmann M; Kleopa K, 2016, 'Gene delivery to oligodendrocytes re-establishes gap junctions and rescues a hypomyelinating leukodystrophy model', in EUROPEAN JOURNAL OF NEUROLOGY, WILEY, pp. 694 - 695, https://www.webofscience.com/api/gateway?GWVersion=2&SrcApp=PARTNER_APP&SrcAuth=LinksAMR&KeyUT=WOS:000431634203169&DestLinkType=FullRecord&DestApp=ALL_WOS&UsrCustomerID=891bb5ab6ba270e68a29b250adbe88d1
    Conference Papers | 2016
    Perera C; Von Jonquieres G; Pinyon J; Parley K; Cederholm J; Julien J-P; Ryan A; Housley G, 2016, 'Phenotyping the differential innervation of the peripherin knockout mouse cochlea', in Proceedings of the Australian Physiological Society, Adelaide, presented at Australian Physiological Society, Adelaide, 04 December 2016 - 07 December 2016
    Conference Abstracts | 2015
    Harasta A; Power JM; von Jonquieres G; Karl T; Drucker DJ; Housley GD; Schneider M; Klugmann M, 2015, 'Septal glucagon-like peptide 1 receptor expression determines suppression of cocaine-induced behaviour', in JOURNAL OF NEUROCHEMISTRY, WILEY-BLACKWELL, AUSTRALIA, Cairns, Vol. 134, pp. 214 - 214, presented at 25th Biennial Meeting of the International-Society-for-Neurochemistry Jointly with the 13th Meeting of the Asian-Pacific-Society-for-Neurochemistry in Conjunction with the 35th Meeting of the Australasian-Neuroscience-Society, AUSTRALIA, Cairns, 23 August 2015 - 27 August 2015, https://www.webofscience.com/api/gateway?GWVersion=2&SrcApp=PARTNER_APP&SrcAuth=LinksAMR&KeyUT=WOS:000360206300522&DestLinkType=FullRecord&DestApp=ALL_WOS&UsrCustomerID=891bb5ab6ba270e68a29b250adbe88d1
    Conference Abstracts | 2015
    Harrison-Tikisci Z; von Jonquieres G; Rowlands B; Klugmann C; Delarue F; Ittner L; Pickford R; Housley G; Rae C; Klugmann M, 2015, 'N-acetylaspartate: genomics, phenomics and metabonomics', in JOURNAL OF NEUROCHEMISTRY, WILEY-BLACKWELL, AUSTRALIA, Cairns, Vol. 134, pp. 141 - 141, presented at 25th Biennial Meeting of the International-Society-for-Neurochemistry Jointly with the 13th Meeting of the Asian-Pacific-Society-for-Neurochemistry in Conjunction with the 35th Meeting of the Australasian-Neuroscience-Society, AUSTRALIA, Cairns, 23 August 2015 - 27 August 2015, https://www.webofscience.com/api/gateway?GWVersion=2&SrcApp=PARTNER_APP&SrcAuth=LinksAMR&KeyUT=WOS:000360206300323&DestLinkType=FullRecord&DestApp=ALL_WOS&UsrCustomerID=891bb5ab6ba270e68a29b250adbe88d1
    Conference Abstracts | 2015
    Jonquieres GV; Mersmann N; Klugmann C; Harrasta A; Klugmann M, 2015, 'Targeting oligodendrocytes in rAAV mediated gene replacement therapy for Canavan disease', in JOURNAL OF NEUROCHEMISTRY, WILEY-BLACKWELL, AUSTRALIA, Cairns, Vol. 134, pp. 289 - 289, presented at 25th Biennial Meeting of the International-Society-for-Neurochemistry Jointly with the 13th Meeting of the Asian-Pacific-Society-for-Neurochemistry in Conjunction with the 35th Meeting of the Australasian-Neuroscience-Society, AUSTRALIA, Cairns, 23 August 2015 - 27 August 2015, https://www.webofscience.com/api/gateway?GWVersion=2&SrcApp=PARTNER_APP&SrcAuth=LinksAMR&KeyUT=WOS:000360206300729&DestLinkType=FullRecord&DestApp=ALL_WOS&UsrCustomerID=891bb5ab6ba270e68a29b250adbe88d1
    Conference Papers | 2013
    von Jonquieres G; Klugmann C; Harrasta A; Klugmann M, 2013, 'DEVELOPMENT OF rAAV VECTORS FOR THE TREATMENT OF LEUKODYSTROPHIES', in JOURNAL OF GENE MEDICINE, WILEY-BLACKWELL, AUSTRALIA, Univ Technol, Sydney, pp. 334 - 335, presented at 8th Meeting of the Australasian-Gene-Therapy-Society, AUSTRALIA, Univ Technol, Sydney, 08 May 2013 - 10 May 2013, https://www.webofscience.com/api/gateway?GWVersion=2&SrcApp=PARTNER_APP&SrcAuth=LinksAMR&KeyUT=WOS:000325102500046&DestLinkType=FullRecord&DestApp=ALL_WOS&UsrCustomerID=891bb5ab6ba270e68a29b250adbe88d1
    Conference Papers | 2012
    Kumari A; Richards LA; Jonquieres G; Knezevic K; O'Brien R; Napier CE; Marks-Bluth J; Pickett H; Pimanda JE; MacKenzie KL, 2012, 'Dyskerin Is Upregulated During Erythroid Differentiation of Human Hematopoietic Progenitor Cells and Hyperactivates Telomerase in Erythroid Precursor Cells', in BLOOD, AMER SOC HEMATOLOGY, GA, Atlanta, presented at 54th Annual Meeting and Exposition of the American-Society-of-Hematology (ASH), GA, Atlanta, 08 December 2012 - 11 December 2012, http://dx.doi.org/10.1182/blood.V120.21.980.980